Spontaneous Complete Remission of Primary Pigmented Adrenocortical Disease1
نویسندگان
چکیده
منابع مشابه
Primary pigmented nodular adrenocortical disease.
Primary pigmented nodular adrenocortical disease (PPNAD) is a rare adrenal tumour causing corticotrophin-independent Cushing's syndrome. It occurs mainly in children and young adults. The histological examination is characterised by small pigmented micronodules on the adrenal cortex. The diagnosis is most often seen in patients with Carney Complex, but it can also occur in isolation. We report ...
متن کاملPigmented Nodular Adrenocortical Disease
Carney complex (CNC) is a multiple endocrine neoplasia (MEN) syndrome associated with other, non-endocrine manifestations such as lentigines, cardiac myxomas and schwannomas. Primary pigmented nodular adrenocortical disease (PPNAD), leading to corticotrophin-independent Cushing’s syndrome is the most frequent endocrine lesion in CNC. The complex has been mapped to 2p16 and 17q22-24, although ad...
متن کاملCushing’s Syndrome Due To Primary Pigmented Nodular Adrenocortical Disease
A 12.5-year-old girl with diabetes mellitus type 1 presented with stunted growth and an increase in body weight. Also, her blood-sugar levels were difficult to manage. An adrenocorticotropin-(ACTH)-independent form of Cushing's syndrome was diagnosed. During the dexamethasone-suppression test, a paradoxical increase in urinary-free cortisol excretion was observed, which is a clear indication of...
متن کاملPrimary pigmented nodular adrenocortical disease and Cushing's syndrome.
Primary pigmented nodular adrenocortical disease (PPNAD) is a form of bilateral adrenocortical hyperplasia that is often associated with corticotrophin (ACTH)-independent Cushing's syndrome (CS) and is characterized by small to normal-sized adrenal glands containing multiple small cortical pigmented nodules (1,2). PPNAD may occur in an isolated form or associated with a multiple neoplasia syndr...
متن کاملPrimary spontaneous complete colporrhexis.
Spontaneous rupture or avulsion of the vagina from the cervix during labour is a rare condition. The term colporrhexis describes this obstetric injury and it is subdi vided into primary or secondary, spontaneous or traumatic, complete or incomplete. Incomplete colporrhexis includes rupture of the vaginal epithelium and the muscularis, whereas complete involves the overlying peritoneum as well....
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: The Journal of Clinical Endocrinology & Metabolism
سال: 1997
ISSN: 0021-972X,1945-7197
DOI: 10.1210/jcem.82.10.4288-8